primary intrahepatic sclerosis syndrome

Primary intrahepatic cirrhosis (Hanot) syndrome, now commonly referred to as primary biliary cirrhosis, also known as chronic non-suppurative destructive cholangitis, cholangitic hepatitis, biliary cirrhosis, and intrahepatic obstructive biliary cirrhosis, refers to a group of syndromes caused by non-specific inflammation and fibrosis of the intrahepatic bile ducts, leading to intrahepatic cholestasis, cirrhosis with nodular hyperplasia.